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Effects of Tributyltin Chloride on Cybrids with or without an ATP Synthase Pathologic Mutation

BACKGROUND: The oxidative phosphorylation system (OXPHOS) includes nuclear chromosome (nDNA)– and mitochondrial DNA (mtDNA)–encoded polypeptides. Many rare OXPHOS disorders, such as striatal necrosis syndromes, are caused by genetic mutations. Despite important advances in sequencing procedures, cau...

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Detalhes bibliográficos
Publicado no:Environ Health Perspect
Main Authors: López-Gallardo, Ester, Llobet, Laura, Emperador, Sonia, Montoya, Julio, Ruiz-Pesini, Eduardo
Formato: Artigo
Idioma:Inglês
Publicado em: National Institute of Environmental Health Sciences 2016
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5010394/
https://ncbi.nlm.nih.gov/pubmed/27129022
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1289/EHP182
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