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Cardiovascular Involvement in Erdheim–Chester Disease: A Case Report and Review of the Literature

Erdheim–Chester disease (ECD) is a rare, multiorgan, non-Langerhans cell histiocytosis of uncertain origin, characterized by systemic xanthogranulomatous infiltration from CD68+CD1a- histiocytes. Skeletal involvement is present in up to 96% of cases with bilateral osteosclerosis of meta-diaphysis of...

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Detalhes bibliográficos
Publicado no:Medicine (Baltimore)
Main Authors: Nicolazzi, Maria Anna, Carnicelli, Annamaria, Fuorlo, Mariella, Favuzzi, Angela Maria Rita, Landolfi, Raffaele
Formato: Artigo
Idioma:Inglês
Publicado em: Wolters Kluwer Health 2015
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4985366/
https://ncbi.nlm.nih.gov/pubmed/26512552
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/MD.0000000000001365
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