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Osteogenesis imperfecta and clubfoot—a rare combination: Case report and review of the literature

BACKGROUND: Osteogenesis imperfecta (OI) is a rare congenital genetic osteodystrophy, which has a prevalence of 1:20,000. OI is caused by the mutation of the COL1A1/COL1A2 genes, leading to a deficit of quality and/or quantity in the synthesis of procollagen-α type 1. Seven different forms of divers...

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Publicat a:Medicine (Baltimore)
Autors principals: Persiani, Pietro, Ranaldi, Filippo Maria, Martini, Lorena, Zambrano, Anna, Celli, Mauro, D’Eufemia, Patrizia, Villani, Ciro
Format: Artigo
Idioma:Inglês
Publicat: Wolters Kluwer Health 2016
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4979856/
https://ncbi.nlm.nih.gov/pubmed/27495102
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/MD.0000000000004505
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