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Histiocytic Sarcoma Associated with Coombs Negative Acute Hemolytic Anemia: A Rare Presentation

Histiocytic sarcoma (HS) rarely involves extranodal sites, such as the spleen. We report a unique pediatric case of massive splenomegaly and refractory Coombs negative hemolytic anemia (CNHA) secondary to HS. The CNHA resolved completely after an emergent splenectomy. Next generation sequencing (NGS...

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Publicado en:Case Rep Oncol Med
Autores principales: Batra, Sandeep, Martin, Stephen C., Nassiri, Mehdi, Qureshi, Amna, Markel, Troy A.
Formato: Artigo
Lenguaje:Inglês
Publicado: Hindawi Publishing Corporation 2016
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4939191/
https://ncbi.nlm.nih.gov/pubmed/27429816
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2016/3179147
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