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Dysferlin Binds SNAREs (Soluble N-Ethylmaleimide-sensitive Factor (NSF) Attachment Protein Receptors) and Stimulates Membrane Fusion in a Calcium-sensitive Manner

Resealing of tears in the sarcolemma of myofibers is a necessary step in the repair of muscle tissue. Recent work suggests a critical role for dysferlin in the membrane repair process and that mutations in dysferlin are responsible for limb girdle muscular dystrophy 2B and Miyoshi myopathy. Beyond m...

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Dades bibliogràfiques
Publicat a:J Biol Chem
Autors principals: Codding, Sara J., Marty, Naomi, Abdullah, Nazish, Johnson, Colin P.
Format: Artigo
Idioma:Inglês
Publicat: American Society for Biochemistry and Molecular Biology 2016
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4938179/
https://ncbi.nlm.nih.gov/pubmed/27226605
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M116.727016
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