Llwytho...

Fatal cases of lipid storage myopathy with carnitine deficiency.

Three patients affected by a progressive myopathy with rapid lethal evolution are presented. Excessive lipid storage was found in type 1 fibres of muscle and in liver, kidney, and myocardium. Carnitine concentrations were markedly reduced in muscle, plasma, and heart, significantly lower in the live...

Disgrifiad llawn

Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Prif Awduron: Cornelio, F, Di Donato, S, Peluchetti, D, Bizze, A, Bertagnolio, B, D'Angelo, A, Wiesmann, U
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: 1977
Pynciau:
Mynediad Ar-lein:https://ncbi.nlm.nih.gov/pmc/articles/PMC492634/
https://ncbi.nlm.nih.gov/pubmed/194020
Tagiau: Ychwanegu Tag
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