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Focal liver hyperplasia in a patient with Alagille syndrome: Diagnostic difficulties. A case report

INTRODUCTION: Alagille syndrome is a multisystem autosomal disorder. The main clinical features are chronic cholestasis due to paucity of intrahepatic bile ducts, which can progress to cirrhosis and liver failure. PRESENTATION OF CASE: A 15 year-old girl with Alagille syndrome was referred for liver...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:Int J Surg Case Rep
Egile Nagusiak: Ennaifer, R., Ben Farhat, L., Cheikh, M., Romdhane, H., Marzouk, Ines, Belhadj, N.
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: Elsevier 2016
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC4916051/
https://ncbi.nlm.nih.gov/pubmed/27322896
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ijscr.2016.03.032
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