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Ectopic mineralization of cartilage and collagen-rich tendons and ligaments in Enpp1(asj-2J) mice

Generalized arterial calcification of infancy (GACI), an autosomal recessive disorder caused by mutations in the ENPP1 gene, manifests with extensive mineralization of the cardiovascular system. A spontaneous asj-2J mutant mouse has been characterized as a model for GACI. Previous studies focused on...

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Détails bibliographiques
Publié dans:Oncotarget
Auteurs principaux: Zhang, Jieyu, Dyment, Nathaniel A., Rowe, David W., Siu, Sarah Y., Sundberg, John P., Uitto, Jouni, Li, Qiaoli
Format: Artigo
Langue:Inglês
Publié: Impact Journals LLC 2016
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC4914264/
https://ncbi.nlm.nih.gov/pubmed/26910915
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.18632/oncotarget.7455
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