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Long-term improvement during tadalafil therapy in a patient with pulmonary hypertension secondary to pulmonary Langerhans cell histiocytosis

Pulmonary arterial hypertension (PAH) secondary to pulmonary Langerhans cell histiocytosis (PLCH) is known to be a relatively common complication and is associated with a poor prognosis. However, the optimal therapeutic approach for these cases remains to be established. A 57-year-old man visited ou...

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Dettagli Bibliografici
Pubblicato in:Respir Med Case Rep
Autori principali: Nemoto, Kenji, Oh-ishi, Shuji, Inui, Toshihide, Nakazawa, Mariko, Hyodo, Kentaro, Nakajima, Masayuki, Kanazawa, Jun, Miura, Yukiko, Takaku, Takio, Minami, Yuko, Hayashihara, Kenji, Saito, Takefumi, Kawabata, Yoshinori
Natura: Artigo
Lingua:Inglês
Pubblicazione: Elsevier 2016
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4913144/
https://ncbi.nlm.nih.gov/pubmed/27330952
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.rmcr.2016.04.008
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