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Rigid spine syndrome

A patient is described with distinctive clinical features including childhood onset of non-progressive muscle weakness, limitation of flexion of the neck and spine, scoliosis, and joint contracture. Muscle biopsy and electromyography showed findings suggestive of a myopathic disorder. The combinatio...

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Autori principali: Goto, Ikuo, Nagasaka, Susumu, Nagara, Hitoshi, Kuroiwa, Yoshigoro
Natura: Artigo
Lingua:Inglês
Pubblicazione: 1979
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC490733/
https://ncbi.nlm.nih.gov/pubmed/438838
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