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Mitochondrial functions in chronic spinal muscular atrophy.

We determined the respiration rate, respiratory control and ADP/O ratios, with different substrates in mitochondria isolated from seven patients with chronic spinal muscular atrophy and compared them with normal human muscle. In all cases studied, a severe alteration of the respiratory control with...

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Autors principals: Gobernado, J M, Gosalvez, M, Cortina, C, Lousa, M, Riva, C, Gimeno, A
Format: Artigo
Idioma:Inglês
Publicat: 1980
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC490598/
https://ncbi.nlm.nih.gov/pubmed/6821580
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