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The cerebellar component of Friedreich’s ataxia

Lack of frataxin in Friedreich’s ataxia (FRDA) causes a complex neurological and pathological phenotype. Progressive atrophy of the dentate nucleus (DN) is a major intrinsic central nervous system lesion. Antibodies to neuron-specific enolase (NSE), calbindin, glutamic acid decarboxylase (GAD), and...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:Acta Neuropathol
Egile Nagusiak: Koeppen, Arnulf H., Davis, Ashley N., Morral, Jennifer A.
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: 2011
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC4890974/
https://ncbi.nlm.nih.gov/pubmed/21638087
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00401-011-0844-9
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