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A novel heterozygous mutation in the ATP6V0A4 gene encoding the V-ATPase a4 subunit in an adult patient with incomplete distal renal tubular acidosis

A 40-year-old Japanese man who had a medical history of hypokalemic periodic paralysis 4 months prior was hospitalized to undergo a cholecystectomy. Hypokalemia, nephrocalcinosis and alkaluria suggesting distal renal tubular acidosis (dRTA) were detected, but metabolic acidosis was not evident. An a...

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Publicado en:Clin Kidney J
Autores principales: Imai, Eri, Kaneko, Shuzo, Mori, Takayasu, Okado, Tomokazu, Uchida, Shinichi, Tsukamoto, Yusuke
Formato: Artigo
Lenguaje:Inglês
Publicado: Oxford University Press 2016
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4886904/
https://ncbi.nlm.nih.gov/pubmed/27274828
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/ckj/sfw008
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