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Safety and Efficacy of Chronic Extended Release Cornstarch Therapy for Glycogen Storage Disease Type I

Background: Glycogen storage disease type I (GSD I) causes severe hypoglycemia during periods of fasting since both glycogenolysis and gluconeogenesis are impaired. Primary treatment in North America consists of cornstarch therapy every 3–4 h. Waxy maize extended release cornstarch was introduced fo...

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Publicado en:JIMD Rep
Main Authors: Ross, Katalin M., Brown, Laurie M., Corrado, Michelle M., Chengsupanimit, Tayoot, Curry, Latravia M., Ferrecchia, Iris A., Porras, Laura Y., Mathew, Justin T., Weinstein, David A.
Formato: Artigo
Idioma:Inglês
Publicado: Springer Berlin Heidelberg 2015
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC4864714/
https://ncbi.nlm.nih.gov/pubmed/26303612
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/8904_2015_488
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