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A Novel ECM1 Splice Site Mutation in Lipoid Proteinosis: Case Report plus Review of the Literature

Lipoid proteinosis (LP) is an autosomal recessive genodermatosis known to be caused by mutations in ECM1. Nonsense and missense mutations are the most common variations in LP. Up to date, only 6 splice site mutations have been observed. We report on a 26-year-old female LP patient from a Turkish con...

Disgrifiad llawn

Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Cyhoeddwyd yn:Mol Syndromol
Prif Awduron: Rey, Linda K., Kohlhase, Jürgen, Möllenhoff, Katrin, Dekomien, Gabriele, Epplen, Jörg T., Hoffjan, Sabine
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: S. Karger AG 2016
Pynciau:
Mynediad Ar-lein:https://ncbi.nlm.nih.gov/pmc/articles/PMC4862396/
https://ncbi.nlm.nih.gov/pubmed/27194970
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1159/000444615
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