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An unusual case of Cowden syndrome associated with ganglioneuromatous polyposis

BACKGROUND: Ganglioneuromatous polyposis (GP) is a very rare disorder which may be associated with other clinical manifestations and syndromes, such as Cowden syndrome, multiple endocrine neoplasia (MEN) type II and neurofibromatosis (NF) 1. The risk for malignant transformation of ganglioneuromas i...

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Détails bibliographiques
Publié dans:Hered Cancer Clin Pract
Auteurs principaux: Pistorius, Steffen, Klink, Barbara, Pablik, Jessica, Rump, Andreas, Aust, Daniela, Garzarolli, Marlene, Schröck, Evelin, Schackert, Hans K.
Format: Artigo
Langue:Inglês
Publié: BioMed Central 2016
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC4862217/
https://ncbi.nlm.nih.gov/pubmed/27168869
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13053-016-0051-8
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