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(99m)Tc-DPD uptake reflects amyloid fibril composition in hereditary transthyretin amyloidosis

AIMS: In transthyretin amyloid (ATTR) amyloidosis various principal phenotypes have been described: cardiac, neuropathic, or a mixed cardiac and neuropathic. In addition, two different types of amyloid fibrils have been identified (type A and type B). Type B fibrils have thus far only been found in...

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Dettagli Bibliografici
Pubblicato in:Ups J Med Sci
Autori principali: Pilebro, Björn, Suhr, Ole B., Näslund, Ulf, Westermark, Per, Lindqvist, Per, Sundström, Torbjörn
Natura: Artigo
Lingua:Inglês
Pubblicazione: Taylor & Francis 2016
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4812053/
https://ncbi.nlm.nih.gov/pubmed/26849806
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3109/03009734.2015.1122687
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