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A Case of Ataxia with Isolated Vitamin E Deficiency Initially Diagnosed as Friedreich's Ataxia

Ataxia with isolated vitamin E deficiency (AVED) is a rare autosomal recessive condition that is caused by a mutation in the alpha tocopherol transfer protein gene. It is almost indistinguishable clinically from Friedreich's ataxia but with appropriate treatment its devastating neurological fea...

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Detalhes bibliográficos
Publicado no:Case Rep Neurol Med
Main Authors: Bonello, Michael, Ray, Partha
Formato: Artigo
Idioma:Inglês
Publicado em: Hindawi Publishing Corporation 2016
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4771890/
https://ncbi.nlm.nih.gov/pubmed/26989534
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2016/8342653
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