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A Sporadic Neonatal Case of Epidermolysis Bullosa Simplex Generalized Intermediate with KRT5 and KRT14 Gene Mutations

Background Epidermolysis bullosa simplex (EBS) is a rare genodermatosis resulting from multiple gene mutations, including KRT5 and KRT14. The clinical expression of the mechanobullous skin fragility disease has not been fully explained by the genotype. Case Description An 11-day-old Japanese newborn...

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Dades bibliogràfiques
Publicat a:AJP Rep
Autors principals: Wakiguchi, Hiroyuki, Hasegawa, Shunji, Maeba, Shinji, Kimura, Sasagu, Ito, Satoko, Tateishi, Hiroshi, Ueda, Kazuhiro, Ohga, Shouichi
Format: Artigo
Idioma:Inglês
Publicat: Thieme Medical Publishers 2016
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4769090/
https://ncbi.nlm.nih.gov/pubmed/26929861
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1055/s-0035-1570386
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