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Birt-Hogg-Dubé syndrome detected incidentally by asymptomatic bilateral pneumothorax in health screening: a case of a young Japanese woman

Birt-Hogg-Dubé syndrome (BHD) is an autosomal dominant disease caused by mutations of germline folliculin (FCLN) mapped in the chromosome 17p11.2 region. BHD commonly accompanies renal tumors, fibrofolliculomas, multiple pulmonary cysts, and spontaneous pneumothorax. We report a case of a young Japa...

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Detalhes bibliográficos
Publicado no:Surg Case Rep
Main Authors: Miura, Kentaro, Kondo, Ryoichi, Kurai, Makoto, Ishii, Keiko
Formato: Artigo
Idioma:Inglês
Publicado em: Springer Berlin Heidelberg 2015
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4747967/
https://ncbi.nlm.nih.gov/pubmed/26943385
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s40792-015-0014-8
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