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Bronchiectasis and homozygous (P1ZZ) alpha 1-antitrypsin deficiency in a young man.

Pulmonary complications of alpha 1-antitrypsin deficiency are most commonly manifested by panlobular emphysema. This report describes histologically proven bronchiectasis in a 21 year old man with massive haemoptysis and homozygous deficiency of alpha 1-antitrypsin. Neither panlobular emphysema nor...

Disgrifiad llawn

Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Prif Awduron: Rodriguez-Cintron, W., Guntupalli, K., Fraire, A. E.
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: 1995
Pynciau:
Mynediad Ar-lein:https://ncbi.nlm.nih.gov/pmc/articles/PMC474302/
https://ncbi.nlm.nih.gov/pubmed/7785020
Tagiau: Ychwanegu Tag
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