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Genetic and functional linkage between ADAMTS superfamily proteins and fibrillin-1: a novel mechanism influencing microfibril assembly and function

Tissue microfibrils contain fibrillin-1 as a major constituent. Microfibrils regulate bioavailability of TGFβ superfamily growth factors and are structurally crucial in the ocular zonule. FBN1 mutations typically cause the Marfan syndrome, an autosomal dominant disorder manifesting with skeletal ove...

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Detalhes bibliográficos
Publicado no:Cell Mol Life Sci
Main Authors: Hubmacher, Dirk, Apte, Suneel S.
Formato: Artigo
Idioma:Inglês
Publicado em: SP Birkhäuser Verlag Basel 2011
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4729447/
https://ncbi.nlm.nih.gov/pubmed/21858451
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00018-011-0780-9
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