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Accelerated Phase of Chediak-Higashi Syndrome at Initial Presentation: A Case Report of an Uncommon Occurrence in a Rare Disorder

Chediak-Higashi syndrome (CHS) is an uncommon and fatal congenital disorder. The characteristic features of CHS are partial oculocutaneous albinism, increased vulnerability to infections, presence of abnormal large granules in leukocytes and an accelerated lymphohistiocytic phase. Accelerated phase...

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Dades bibliogràfiques
Publicat a:J Clin Diagn Res
Autors principals: Jaiswal, Pooja, Yadav, Yogesh Kumar, Bhasker, Nilam, Kushwaha, Rashmi
Format: Artigo
Idioma:Inglês
Publicat: JCDR Research and Publications (P) Limited 2015
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4717716/
https://ncbi.nlm.nih.gov/pubmed/26816903
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.7860/JCDR/2015/15430.6906
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