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Proteus syndrome: evaluation of the immunological profile

Proteus syndrome (PS) is an extremely rare and complex disease characterized by malformations and overgrowth of different tissues. Prognosis of affected patients may be complicated by premature death, mostly due to pulmonary embolism and respiratory failure. To date, immunological data in Proteus sy...

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Bibliografski detalji
Izdano u:Orphanet J Rare Dis
Glavni autori: Lougaris, Vassilios, Salpietro, Vincenzo, Cutrupi, Maricia, Baronio, Manuela, Moratto, Daniele, Pizzino, M. R., Mankad, Kshitij, Briuglia, Silvana, Salpietro, Carmelo, Plebani, Alessandro
Format: Artigo
Jezik:Inglês
Izdano: BioMed Central 2016
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC4711050/
https://ncbi.nlm.nih.gov/pubmed/26758562
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-015-0381-z
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