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The Unfolded Protein Response and the Role of Protein Disulfide Isomerase in Neurodegeneration

The maintenance and regulation of proteostasis is a critical function for post-mitotic neurons and its dysregulation is increasingly implicated in neurodegenerative diseases. Despite having different clinical manifestations, these disorders share similar pathology; an accumulation of misfolded prote...

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Detalhes bibliográficos
Publicado no:Front Cell Dev Biol
Main Authors: Perri, Emma R., Thomas, Colleen J., Parakh, Sonam, Spencer, Damian M., Atkin, Julie D.
Formato: Artigo
Idioma:Inglês
Publicado em: Frontiers Media S.A. 2016
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4705227/
https://ncbi.nlm.nih.gov/pubmed/26779479
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fcell.2015.00080
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