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Iron Homeostasis and Inflammatory Status in Mice Deficient for the Cystic Fibrosis Transmembrane Regulator

BACKGROUND: Cystic Fibrosis (CF) is a frequent and lethal autosomal recessive disease caused by mutations in the gene encoding the Cystic Fibrosis Transmembrane Conductance Regulator (CFTR). Patients with CF suffer from chronic infections and severe inflammation, which lead to progressive pulmonary...

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Detalhes bibliográficos
Publicado no:PLoS One
Main Authors: Deschemin, Jean-Christophe, Allouche, Sarah, Brouillard, Franck, Vaulont, Sophie
Formato: Artigo
Idioma:Inglês
Publicado em: Public Library of Science 2015
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4699203/
https://ncbi.nlm.nih.gov/pubmed/26709821
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0145685
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