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Neutrophil activation during attacks in patients with hereditary angioedema due to C1-inhibitor deficiency

BACKGROUND: Earlier studies have shown that the absolute number of neutrophil granulocytes (NGs) may increase during attack of hereditary angioedema due to C1-inhibitor deficiency (C1-INH-HAE). Whether NGs undergo activation during attack has not yet been investigated. However, as neutrophil elastas...

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Dettagli Bibliografici
Pubblicato in:Orphanet J Rare Dis
Autori principali: Veszeli, Nóra, Csuka, Dorottya, Zotter, Zsuzsanna, Imreh, Éva, Józsi, Mihály, Benedek, Szabolcs, Varga, Lilian, Farkas, Henriette
Natura: Artigo
Lingua:Inglês
Pubblicazione: BioMed Central 2015
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4674948/
https://ncbi.nlm.nih.gov/pubmed/26654922
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-015-0374-y
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