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Alagille Syndrome Mimicking Biliary Atresia in Early Infancy

Alagille syndrome may mimic biliary atresia in early infancy. Since mutations in JAG1 typical for Alagille syndrome type 1 have also been found in biliary atresia, we aimed to identify JAG1 mutations in newborns with proven biliary atresia (n = 72). Five biliary atresia patients with cholestasis, on...

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Detalhes bibliográficos
Publicado no:PLoS One
Main Authors: Dědič, Tomáš, Jirsa, Milan, Keil, Radan, Rygl, Michal, Šnajdauf, Jiri, Kotalová, Radana
Formato: Artigo
Idioma:Inglês
Publicado em: Public Library of Science 2015
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4664419/
https://ncbi.nlm.nih.gov/pubmed/26618708
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0143939
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