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Ciliary disorientation: a possible variant of primary ciliary dyskinesia.

Random ciliary orientation has recently been proposed as a variant of primary ciliary dyskinesia. We report a 12 year old boy with all the features of primary ciliary dyskinesia and absent nasal mucociliary clearance in whom repeated biopsies of the nasal epithelium showed normal ciliary beat freque...

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Detalhes bibliográficos
Publicado no:Thorax
Main Authors: Rutman, A, Cullinan, P, Woodhead, M, Cole, P J, Wilson, R
Formato: Artigo
Idioma:Inglês
Publicado em: BMJ Publishing Group 1993
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC464673/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/8153929/
https://ncbi.nlm.nih.govhttps://doi.org/10.1136/thx.48.7.770
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