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Pitfalls in molecular diagnosis of 21-hydroxylase deficiency in congenital adrenal hyperplasia

Congenital adrenal hyperplasia (CAH) is a putative error of metabolism with autosomal recessive heredity pattern. The main manifestations of classic form of CAH are salt-wasting, dehydration and simple virilization in both sexes and ambiguous genitalia in female gender. 21-hyroxylase (CYP21A2) impai...

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書目詳細資料
發表在:Adv Biomed Res
Main Authors: Kolahdouz, Mahsa, Mohammadi, Zahra, Kolahdouz, Parisa, Tajamolian, Masoud, Khanahmad, Hossein
格式: Artigo
語言:Inglês
出版: Medknow Publications & Media Pvt Ltd 2015
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在線閱讀:https://ncbi.nlm.nih.gov/pmc/articles/PMC4617158/
https://ncbi.nlm.nih.gov/pubmed/26605228
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/2277-9175.164009
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