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Irreversible Respiratory Failure in a Full-Term Infant with Features of Pulmonary Interstitial Glycogenosis as Well as Bronchopulmonary Dysplasia

Pulmonary interstitial glycogenosis (PIG) is a rare interstitial lung disease in the newborns. We report on the clinical presentation and pathological findings of a full-term male infant with pulmonary hypertension requiring extracorporeal membrane oxygenation (ECMO). An open lung biopsy demonstrate...

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Publicat a:AJP Rep
Autors principals: Jiskoot-Ermers, Maresa E. C., Antonius, Tim A. J., Looijen-Salamon, Monika G., Wijnen, Marc H. W. A., Loza, Bettina F., Heijst, Arno F. J. van
Format: Artigo
Idioma:Inglês
Publicat: Thieme Medical Publishers 2015
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4603843/
https://ncbi.nlm.nih.gov/pubmed/26495172
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1055/s-0035-1551674
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