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Cystathionine Levels in Patients With Huntington Disease

Background: Recently a profound depletion of cystathionine γ-lyase (CSE), the principal enzyme involved in the generation of cysteine from cystathionine, was shown in Huntington disease (HD) patients and several transgenic HD mouse models. We therefore hypothesized that blood and urine cystathionine...

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Библиографические подробности
Опубликовано в: :PLoS Curr
Главные авторы: Aziz, N.A., Onkenhout, W., Kerstens, H.J., Roos, Raymund A.C.
Формат: Artigo
Язык:Inglês
Опубликовано: Public Library of Science 2015
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Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC4582017/
https://ncbi.nlm.nih.gov/pubmed/26435880
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/currents.hd.c63b441d04bb6738c0234f91c2b3e312
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