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Myocardial Fibrosis Burden Predicts Left Ventricular Ejection Fraction and Is Associated With Age and Steroid Treatment Duration in Duchenne Muscular Dystrophy

BACKGROUND: Patients with Duchenne muscular dystrophy exhibit progressive cardiac and skeletal muscle dysfunction. Based on prior data, cardiac dysfunction in Duchenne muscular dystrophy patients may be influenced by myocardial fibrosis and steroid therapy. We examined the longitudinal relationship...

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Dades bibliogràfiques
Publicat a:J Am Heart Assoc
Autors principals: Tandon, Animesh, Villa, Chet R., Hor, Kan N., Jefferies, John L., Gao, Zhiqian, Towbin, Jeffrey A., Wong, Brenda L., Mazur, Wojciech, Fleck, Robert J., Sticka, Joshua J., Benson, D. Woodrow, Taylor, Michael D.
Format: Artigo
Idioma:Inglês
Publicat: Blackwell Publishing Ltd 2015
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4579941/
https://ncbi.nlm.nih.gov/pubmed/25814625
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1161/JAHA.114.001338
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