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Clinical and Pathological Findings of a Fatal Systemic Capillary Leak Syndrome (Clarkson Disease): A Case Report

Systemic capillary leak syndrome (SCLS) is a rare disorder with episodes of hypotension, hypoalbuminemia, and hemoconcentration. During attacks endothelial hyperpermeability results in leakage of plasma proteins into the interstitial space. Attacks vary in severity and may be lethal. A 49-year-old p...

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Detalhes bibliográficos
Publicado no:Medicine (Baltimore)
Main Authors: Zancanaro, Andrea, Serafini, Francesco, Fantin, Giuseppe, Murer, Bruno, Cicardi, Marco, Bonanni, Luca, Dalla Vestra, Michele, Scanferlato, Mauro, Mazzanti, Giovanni, Presotto, Fabio
Formato: Artigo
Idioma:Inglês
Publicado em: Wolters Kluwer Health 2015
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4553957/
https://ncbi.nlm.nih.gov/pubmed/25738482
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/MD.0000000000000591
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