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Measuring Neuromuscular Junction Functionality in the SOD1(G93A) Animal Model of Amyotrophic Lateral Sclerosis

Amyotrophic lateral sclerosis (ALS) is a fatal neurodegenerative disease that leads to motor neuron degeneration, alteration in neuromuscular junctions (NMJs), muscle atrophy, and paralysis. To investigate the NMJ functionality in ALS we tested, in vitro, two innervated muscle types excised from SOD...

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Dettagli Bibliografici
Pubblicato in:Ann Biomed Eng
Autori principali: Rizzuto, Emanuele, Pisu, Simona, Musarò, Antonio, Del Prete, Zaccaria
Natura: Artigo
Lingua:Inglês
Pubblicazione: Springer US 2015
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4516896/
https://ncbi.nlm.nih.gov/pubmed/25631208
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s10439-015-1259-x
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