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Immune status of patients with inherited bone marrow failure syndromes

Immune function abnormalities have been reported in patients with Fanconi anemia (FA), dyskeratosis congenita (DC) and, rarely, in Shwachman-Diamond syndrome (SDS) and Diamond-Blackfan anemia (DBA), but large systematic studies are lacking. We assessed immunological parameters in 118 patients with t...

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Detalhes bibliográficos
Publicado no:Am J Hematol
Main Authors: Giri, Neelam, Alter, Blanche P, Penrose, Keri, Falk, Roni T, Pan, Yuanji, Savage, Sharon A, Williams, Marcus, Kemp, Troy J, Pinto, Ligia A
Formato: Artigo
Idioma:Inglês
Publicado em: 2015
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4509864/
https://ncbi.nlm.nih.gov/pubmed/25963299
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/ajh.24046
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