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Refsum Disease Presenting with a Late-Onset Leukodystrophy

Adult Refsum disease is an autosomal recessive peroxisomal disorder characterized by phytanic acid storage. Clinical symptoms usually begin in late childhood before the age of 20. Typical clinical presentation includes nyctalopia caused by retinitis pigmentosa, and anosmia. After 10–15 years, deafne...

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Bibliografiske detaljer
Udgivet i:JIMD Rep
Main Authors: Bompaire, Flavie, Marcaud, Véronique, Trionnaire, Emmanuelle Le, Sedel, Frédéric, Levade, Thierry
Format: Artigo
Sprog:Inglês
Udgivet: Springer Berlin Heidelberg 2015
Fag:
Online adgang:https://ncbi.nlm.nih.gov/pmc/articles/PMC4501234/
https://ncbi.nlm.nih.gov/pubmed/25604618
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/8904_2014_355
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