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Recombinant Human C1 Esterase Inhibitor in the Management of Hereditary Angioedema

Hereditary angioedema (HAE), a rare autosomal dominant genetic disorder, is caused by a deficiency in functional C1 esterase inhibitor (C1-INH). This potentially life-threatening condition manifests as recurrent attacks of subcutaneous and submucosal swelling of the skin, gastrointestinal tract and...

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Publicado en:Clin Drug Investig
Autor principal: Riedl, Marc
Formato: Artigo
Lenguaje:Inglês
Publicado: Springer International Publishing 2015
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4488495/
https://ncbi.nlm.nih.gov/pubmed/26091744
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s40261-015-0300-z
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