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Spontaneous Dissection of the Renal Artery in Vascular Ehlers-Danlos Syndrome

Ehlers-Danlos syndrome (EDS) is a rare heterogeneous group of connective tissue disorders. The vascular type (vEDS) is an autosomal dominant disorder caused by heterozygous mutations in the COL3A1 gene predisposing to premature arterial, intestinal, or uterine rupture. We report a case of a 38-year-...

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Publicat a:Case Rep Crit Care
Autors principals: Pereira, Filipa, Cardoso, Teresa, Sá, Paula
Format: Artigo
Idioma:Inglês
Publicat: Hindawi Publishing Corporation 2015
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4484843/
https://ncbi.nlm.nih.gov/pubmed/26175915
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2015/804252
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