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Di-sulfated Keratan Sulfate as a Novel Biomarker for Mucopolysaccharidosis II, IVA, and IVB

Keratan sulfate (KS) is a storage material in mucopolysaccharidosis IV (MPS IV). However, no detailed analysis has been reported on subclasses of KS: mono-sulfated KS and di-sulfated KS. We established a novel method to distinguish and quantify mono- and di-sulfated KS using liquid chromatography–ta...

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Detalhes bibliográficos
Publicado no:JIMD Rep
Main Authors: Shimada, Tsutomu, Tomatsu, Shunji, Mason, Robert W., Yasuda, Eriko, Mackenzie, William G., Hossain, Jobayer, Shibata, Yuniko, Montaño, Adriana M., Kubaski, Francyne, Giugliani, Roberto, Yamaguchi, Seiji, Suzuki, Yasuyuki, Orii, Kenji E., Fukao, Toshiyuki, Orii, Tadao
Formato: Artigo
Idioma:Inglês
Publicado em: Springer Berlin Heidelberg 2015
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4470954/
https://ncbi.nlm.nih.gov/pubmed/25712379
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/8904_2014_330
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