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Nonhepatic hyperammonemic encephalopathy due to undiagnosed urea cycle disorder

Ornithine transcarbamoylase deficiency is the most common inherited urea cycle disorder. In adults, its phenotypes are diverse. In asymptomatic patients with late presentations, symptom onset is often associated with a precipitating factor. We present a case of a woman with urea cycle disorder diagn...

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Dades bibliogràfiques
Publicat a:Proc (Bayl Univ Med Cent)
Autors principals: Mahmood, Tashfeen, Nugent, Kenneth
Format: Artigo
Idioma:Inglês
Publicat: Baylor Health Care System 2015
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4462228/
https://ncbi.nlm.nih.gov/pubmed/26130895
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