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Dyskeratosis Congenita Without Oral Involvement: A Rare Hereditary Disease

Dyskeratosis congenita (DC) is a rare, progressive, multi-system, inherited disorder of telomere biology, first described in 1906 as the Zinsser–Engman–Cole syndrome. The condition presents with the classic triad of nail dystrophy, reticulate skin pigmentation, and oral leukoplakia. Variable somatic...

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Detalhes bibliográficos
Publicado no:Oman Med J
Main Authors: Iraji, Fariba, Jamshidi, Kioumars, Pourazizi, Mohsen, Abtahi-Naeini, Bahareh
Formato: Artigo
Idioma:Inglês
Publicado em: OMJ 2015
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4459155/
https://ncbi.nlm.nih.gov/pubmed/26171129
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.5001/omj.2015.44
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