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Genetic Testing in the Diagnosis of Primary Ciliary Dyskinesia: State-of-the-Art and Future Perspectives

Primary ciliary dyskinesia (PCD) is a heterogeneous autosomal recessive condition affecting around 1:15,000. In people with PCD, microscopic motile cilia do not move normally resulting in impaired clearance of mucus and debris leading to repeated sinopulmonary infection. If diagnosis is delayed, per...

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Detalhes bibliográficos
Publicado no:J Clin Med
Main Authors: Collins, Samuel A., Walker, Woolf T., Lucas, Jane S.
Formato: Artigo
Idioma:Inglês
Publicado em: MDPI 2014
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4449687/
https://ncbi.nlm.nih.gov/pubmed/26237387
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/jcm3020491
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