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Analysis of the genetic basis of periodic fever with aphthous stomatitis, pharyngitis, and cervical adenitis (PFAPA) syndrome

PFAPA syndrome is the most common autoinflammatory syndrome in children from Western countries. In spite of its strong familial clustering, its genetic basis and inheritance pattern are still unknown. We performed a comprehensive genetic study on 68 individuals from 14 families. Linkage analysis sug...

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Publicat a:Sci Rep
Autors principals: Gioia, Silvio Alessandro Di, Bedoni, Nicola, von Scheven-Gête, Annette, Vanoni, Federica, Superti-Furga, Andrea, Hofer, Michaël, Rivolta, Carlo
Format: Artigo
Idioma:Inglês
Publicat: Nature Publishing Group 2015
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4437314/
https://ncbi.nlm.nih.gov/pubmed/25988833
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/srep10200
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