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An uncommon presentation of EBV-driven HLH. Primary or secondary? An ongoing dilemma

Haemophagocytic lymphohistiocytosis (HLH) is a potentially fatal syndrome, mainly characterised by dysregulated immune activation. The syndrome is related to a genetic cause, in the classic primary form, or to identified triggers such as infections, malignancy or rheumatological processes, in the cl...

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Detalhes bibliográficos
Publicado no:BMJ Case Rep
Main Authors: Serrão, Tânia, Dias, Alexandra, Nunes, Pedro, Figueiredo, António
Formato: Artigo
Idioma:Inglês
Publicado em: BMJ Publishing Group 2015
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4434350/
https://ncbi.nlm.nih.gov/pubmed/25948855
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2015-209615
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