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Marfan syndrome: defective synthesis, secretion, and extracellular matrix formation of fibrillin by cultured dermal fibroblasts.

We studied the synthesis, secretion, and aggregation into the extracellular matrix of fibrillin by dermal fibroblasts from 26 probands with the Marfan syndrome. Cells from seven probands synthesized approximately half the normal amount of fibrillin when compared with intrafamilial or unrelated contr...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: Milewicz, D M, Pyeritz, R E, Crawford, E S, Byers, P H
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: 1992
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC442822/
https://ncbi.nlm.nih.gov/pubmed/1729284
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