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Multifocal Retinopathy in Dachshunds with CLN2 Neuronal Ceroid Lipofuscinosis

The CLN2 form of neuronal ceroid lipofuscinosis is an autosomal recessively inherited lysosomal storage disease that is characterized by progressive vision loss culminating in blindness, cognitive and motor decline, neurodegeneration, and premature death. CLN2 disease results from mutations in the g...

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Détails bibliographiques
Publié dans:Exp Eye Res
Auteurs principaux: Whiting, Rebecca E.H., Pearce, Jacqueline W., Castaner, Leilani J., Jensen, Cheryl A., Katz, Rebecca J., Gilliam, Douglas H., Katz, Martin L.
Format: Artigo
Langue:Inglês
Publié: 2015
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC4426040/
https://ncbi.nlm.nih.gov/pubmed/25697710
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.exer.2015.02.012
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