Peroxisomal fatty acid beta-oxidation in relation to the accumulation of very long chain fatty acids in cultured skin fibroblasts from patients with Zellweger syndrome and other peroxisomal disorders.

The peroxisomal oxidation of the long chain fatty acid palmitate (C16:0) and the very long chain fatty acids lignocerate (C24:0) and cerotate (C26:0) was studied in freshly prepared homogenates of cultured skin fibroblasts from control individuals and patients with peroxisomal disorders. The peroxis...

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Pubblicato in:	J Clin Invest
Autori principali:	Wanders, R J, van Roermund, C W, van Wijland, M J, Schutgens, R B, Heikoop, J, van den Bosch, H, Schram, A W, Tager, J M
Natura:	Artigo
Lingua:	Inglês
Pubblicazione:	American Society for Clinical Investigation 1987
Soggetti:	Research Article
Accesso online:	https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC442453/ https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/3680527/ https://ncbi.nlm.nih.govhttps://doi.org/10.1172/JCI113271
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