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Prevalence of hereditary angioedema in untested first-degree blood relatives of known subjects with hereditary angioedema

Hereditary angioedema (HAE) is a rare autosomal-dominant disease characterized by recurring attacks of nonpruritic, nonpitting edema caused by an inherited deficiency or dysfunction of C1 esterase inhibitor (C1 INH). Symptoms can present years before an accurate diagnosis is made. The objective of t...

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Dettagli Bibliografici
Pubblicato in:Allergy Asthma Proc
Autori principali: Riedl, Marc A., Lumry, William R., Busse, Paula, Levy, Howard, Steele, Tamara, Dayno, Jeffrey, Li, H. Henry
Natura: Artigo
Lingua:Inglês
Pubblicazione: OceanSide Publications, Inc. 2015
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4405600/
https://ncbi.nlm.nih.gov/pubmed/25803135
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2500/aap.2015.36.3833
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