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A Unique Case Involving a Female Patient with Upshaw-Schulman Syndrome: Low Titers of Antibodies against ADAMTS13 prior to Pregnancy Disappeared after Successful Delivery

BACKGROUND: Upshaw-Schulman syndrome (USS) is usually suspected based on severe deficiency of ADAMTS13 activity without ADAMTS13 antibody, but the definitive diagnosis is made by ADAMTS13 gene analysis. We present a unique case of USS with low titers of ADAMTS13 antibodies before pregnancy. Interest...

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Bibliografski detalji
Izdano u:Transfus Med Hemother
Glavni autori: Ogawa, Yoshiyuki, Matsumoto, Masanori, Sadakata, Hisanobu, Isonishi, Ayami, Kato, Seiji, Nojima, Yoshihisa, Fujimura, Yoshihiro
Format: Artigo
Jezik:Inglês
Izdano: S. Karger GmbH 2015
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Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC4404895/
https://ncbi.nlm.nih.gov/pubmed/25960717
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1159/000370225
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